Idiopathic Pleuroparenchymal Fibroelastosis

MANAGEMENT

DISEASE AND SYMPTOM MANAGEMENT

Corticosteroids9,10

Although there are no currently approved therapies, corticosteroids are often used empirically to treat idiopathic PPFE. Its efficacy is unknown.

See also

Patient Case Study 1

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Bridging Educational Gaps in ILD

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Interstitial lung disease in systemic sclerosis with a focus on chest CT

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