Idiopathic Pleuroparenchymal Fibroelastosis

MANAGEMENT

DISEASE AND SYMPTOM MANAGEMENT

Corticosteroids9,10

Although there are no currently approved therapies, corticosteroids are often used empirically to treat idiopathic PPFE. Its efficacy is unknown.

See also

Man smiling

Test your knowledge

Take the test 

Bridging gaps in ILD education image

Bridging educational gaps in ILD

Learn more 

Interstitial lung disease in systemic sclerosis with a focus on chest CT

Media library

See media